ANKMJ
Ankyra Medical Journal

Ankyra Medical Journal (AnkMJ), formerly known as the Journal of Translational and Practical Medicine, regularly publishes international quality issues in the field of Medicine in the light of current information.

eISSN: 3023-655X
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Letter to the Editor
Complex spinal case associated with Angelman syndrome
Abstract
Angelman syndrome may be complicated by rapidly progressive neuromuscular scoliosis. We report a 14-year-old girl with three months of worsening deformity and new right-leg weakness, with double curves ~80°. Posterior instrumented correction was performed with multimodal intraoperative neuromonitoring; baseline signals were obtained supine and rechecked after prone positioning, guiding safe correction. Early postoperative radiographs showed improved alignment. This case underscores the need for early recognition, individualized surgical planning, and routine neuromonitoring to minimize neurologic risk in Angelman syndrome–associated scoliosis.

Keywords : Angelman syndrome, complex spine surgery, intraoperative neuromonitoring, neuromuscular disorder, scoliosis

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Article available in :
Volume 4, Issue 4, 2025
Page : 93-94
https://doi.org/10.51271/ANKMJ-0056
Article Information
Received : 02 Eki 2025
Accepted : 18 Eki 2025
Published : 19 Eki 2025
Corresponding Author :

Murat Baloğlu: Department of Neurosurgery, Eskişehir City Hospital, Eskişehir, Turkiye

[email protected]
Citation : Baloğlu M. Complex spinal case associated with Angelman syndrome. Ank Med J. 2025;4(4):93-94.

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